Outcomes of Cochlear Implantation in Patients With Superficial Siderosis: A Systematic Review and Narrative Synthesis

Journal of International Advanced Otology

Chaudhry, A., Chaudhry, D., et al. (2020).

Journal of International Advanced Otology, 16(3), 443-455.

This systematic review investigates the effects of cochlear implantation in individuals with superficial siderosis.

No funding received



Database inception up to March 21, 2020

All study designs, including case-control, cohort, and case series studies

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Results indicated that 70.45% of cochlear implants for superficial siderosis (SS) had improved hearing outcomes at some point in time and 50% of cochlear implants for SS demonstrated sustained benefit at the last follow-up, ranging from three months to 84 months. "It is difficult to predict the longevity of benefit because of the progressive nature of the disease or the patients in whom it might be beneficial as preoperative investigations are inadequate prognosticators" (p. 454). 

Although the majority of included studies focused on adults, one of the studies included school-aged children. Overall results indicated that 70.45% of cochlear implants for superficial siderosis (SS) had improved hearing outcomes at some point in time and 50% of cochlear implants for SS demonstrated sustained benefit at the last follow-up, ranging from three months to 84 months. "It is difficult to predict the longevity of benefit because of the progressive nature of the disease or the patients in whom it might be beneficial as preoperative investigations are inadequate prognosticators" (p. 454).