Systematic Review of Current Audiological Treatment Options for Patients With Treacher Collins Syndrome (TCS) and Surgical and Audiological Experiences of an Otorhinolaryngologist With TCS
Journal of Personalized Medicine
Marinac, I., Trotić, R., et al. (2024).
Journal of Personalized Medicine, 14(1), 81.
This systematic review examines the effect of any kind of hearing device on a variety of outcomes (e.g., audiological, language acquisition, hearing ability, quality of life) for individuals with Treacher Collins Syndrome (TCS).
No funding received
June 2013 to June 2023
All study designs. Excludes systematic reviews, letters, editorials, and comments.
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The majority of studies (eight out of nine) investigated the effects of bone-conduction devices on individuals with TCS. Bone-conduction hearing devices demonstrated an average improvement in auditory capacity of approximately 30 dB and increased speech comprehension. One study reporting Speech, Spatial, and Qualities of Hearing questionnaire (SSQ) scores found considerably improved quality of life three months post-device implantation. <span style="color: #333333;">These findings are based on Level IV to V Evidence. They should be interpreted with caution due to small sample sizes across a limited number of research articles and to differences between studies regarding selected outcome measures and treatments. Additional research is indicated. </span>
One study investigated the effects of conventional hearing aids on individuals with TCS. Hearing aids demonstrated an average improvement in auditory capacity of approximately 30 dB and increased speech comprehension. These findings are based on Level IV to V Evidence. They should be interpreted with caution due to small sample sizes across a limited number of research articles and to differences between studies regarding selected outcome measures and treatments. Additional research is indicated.
One case study investigated the effects of an active middle ear implant (i.e., Vibrant Soundbridge) on an individual with TCS. The Vibrant Soundbridge demonstrated improved speech intelligibility and no deterioration of natural hearing. These findings are based on Level IV to V Evidence. They should be interpreted with caution due to small sample sizes across a limited number of research articles and to differences between studies regarding selected outcome measures and treatments. Additional research is indicated.
