Hearing Loss in Inner Ear and Systemic Autoimmune Disease: A Systematic Review of Post-Cochlear Implantation Outcomes

Laryngoscope Investigative Otolaryngology

Lee, J., Biggs, K., et al. (2021).

Laryngoscope Investigative Otolaryngology, 6(3), 469-487.

This systematic review investigates the effects of cochlear implantation on audiometric outcomes in children or adults with systemic or inner ear autoimmune hearing loss.

Not stated



From database inception to January 16, 2021

Experimental or observational designs reporting post-implantation outcomes

29

Studies using multiple heterogeneous audiological measures reported improved post-cochlear implantation (CI) hearing outcomes as compared to pre-operative hearing in the majority of patients with primary and secondary autoimmune inner ear disease (AIED). None of the included studies included patient-reported outcomes. Patients with secondary AIED were at a higher risk of poor CI response; however, no additional perioperative complication risks were reported compared to other CI recipients. The authors conclude that CI may provide a long-term beneficial option for patients with AIED.